Catastrophic antiphospholipid syndrome: international consensus statement on classification criteria and treatment guidelines | Semantic Scholar

An international registry of patients with catastrophic APS (CAPS Registry) was created in 2000 by the European Forum on aPL, and the analysis of this registry has allowed the characterization of the clinical and laboratory features of the catastrophic APs as well as the establishment of preliminary criteria for its classification and guidelines for its management.

Although less than 1% of patients with the antiphospholipid syndrome develop the catastrophic variant, its potentially lethal outcome emphasizes its importance in clinical medicine today and it is expected that the periodical analysis of these data will allow us to increase the authors' knowledge of this condition.