Genetic variants of Wnt transcription factor TCF-4 (TCF7L2) putative promoter region are associated with small intestinal Crohn's disease - PubMed
doi: 10.1371/journal.pone.0004496. Epub 2009 Feb 16.
Irmgard Kübler, Mathias Chamaillard, Elke Schaeffeler, Walter Reinisch, Guoxing Wang, Julia Beisner, Alexander Teml, Laurent Peyrin-Biroulet, Stefan Winter, Klaus R Herrlinger, Paul Rutgeerts, Séverine Vermeire, Rachel Cooney, Klaus Fellermann, Derek Jewell, Charles L Bevins, Matthias Schwab, Eduard F Stange, Jan Wehkamp
Affiliations
- PMID: 19221600
- PMCID: PMC2637978
- DOI: 10.1371/journal.pone.0004496
Genetic variants of Wnt transcription factor TCF-4 (TCF7L2) putative promoter region are associated with small intestinal Crohn's disease
Maureen J Koslowski et al. PLoS One. 2009.
Abstract
Reduced expression of Paneth cell antimicrobial alpha-defensins, human defensin (HD)-5 and -6, characterizes Crohn's disease (CD) of the ileum. TCF-4 (also named TCF7L2), a Wnt signalling pathway transcription factor, orchestrates Paneth cell differentiation, directly regulates the expression of HD-5 and -6, and was previously associated with the decrease of these antimicrobial peptides in a subset of ileal CD. To investigate a potential genetic association of TCF-4 with ileal CD, we sequenced 2.1 kb of the 5' flanking region of TCF-4 in a small group of ileal CD patients and controls (n = 10 each). We identified eight single nucleotide polymorphisms (SNPs), of which three (rs3814570, rs10885394, rs10885395) were in linkage disequilibrium and found more frequently in patients; one (rs3814570) was thereby located in a predicted regulatory region. We carried out high-throughput analysis of this SNP in three cohorts of inflammatory bowel disease (IBD) patients and controls. Overall 1399 healthy individuals, 785 ulcerative colitis (UC) patients, 225 CD patients with colonic disease only and 784 CD patients with ileal involvement were used to determine frequency distributions. We found an association of rs3814570 with ileal CD but neither with colonic CD or UC, in a combined analysis (allele positivity: OR 1.27, 95% CI 1.07 to 1.52, p = 0.00737), which was the strongest in ileal CD patients with stricturing behaviour (allele frequency: OR 1.32, 95% CI 1.08 to1.62, p = 0.00686) or an additional involvement of the upper GIT (allele frequency: OR 1.38, 95% CI 1.03 to1.84, p = 0.02882). The newly identified genetic association of TCF-4 with ileal CD provides evidence that the decrease in Paneth cell alpha-defensins is a primary factor in disease pathogenesis.
Conflict of interest statement
Competing Interests: MJK, JB, EFS and JW have a pending patent application regarding TCF-4 SNP detection.
Figures

Sequencing of a 2.1 kb upstream region was performed in 10 healthy controls and 10 patients with ileal Crohn's disease. Putative regulatory regions were determined using promoter prediction software. Likely and marginal prediction sites are depicted as red boxes (upper panel). Relative location of identified variants is marked via grey dashes (upper part) and their allele frequency is demonstrated via bars for controls as well as patients (lower part).

Both colour schemes (a and b) illustrate the linkage disequilibria. The variants are listed in the upper part of a and b, respectively. Haplotypes for TCF-4 (TCF7L2) rs3814570 (SNP1), rs10885394 (SNP2), rs10885395 (SNP3) and SNPs associated with diabetes in the Vienna cohort are shown in a. A missing number for D′ or r2 equals 1. Figure 2b: HapMap data based haplotype blocks and linkage disequilibria (LD) for TCF-4 (TCF7L2) polymorphisms. The intensity of red colouring in b is proportional to the extent of D′ or r 2 respectively and a missing number for each of them equals. The observed SNP in the putative promoter region is not part of any significant haplotype block.

Odds ratios and confidence intervals for the different comparisons are shown. The frequency distribution of rs3814570 was analyzed in different cohorts and combined samples: odds ratios and 95% confidence interval for allele frequency (upper panel) and allele positivity (amount of all T- allele carriers, lower panel) are shown for patients with ulcerative colitis (UC) (left panel), Crohn's disease (CD) patients with solely colonic involvement (L2, middle panel) and finally patients classified as either L1 (solely ileal) or L3 (ileal and colonic involvement) (right panel) compared to healthy control individuals.
Similar articles
-
The Paneth cell alpha-defensin deficiency of ileal Crohn's disease is linked to Wnt/Tcf-4.
Wehkamp J, Wang G, Kübler I, Nuding S, Gregorieff A, Schnabel A, Kays RJ, Fellermann K, Burk O, Schwab M, Clevers H, Bevins CL, Stange EF. Wehkamp J, et al. J Immunol. 2007 Sep 1;179(5):3109-18. doi: 10.4049/jimmunol.179.5.3109. J Immunol. 2007. PMID: 17709525
-
Koslowski MJ, Teltschik Z, Beisner J, Schaeffeler E, Wang G, Kübler I, Gersemann M, Cooney R, Jewell D, Reinisch W, Vermeire S, Rutgeerts P, Schwab M, Stange EF, Wehkamp J. Koslowski MJ, et al. PLoS Genet. 2012;8(2):e1002523. doi: 10.1371/journal.pgen.1002523. Epub 2012 Feb 23. PLoS Genet. 2012. PMID: 22393312 Free PMC article.
-
Beisner J, Teltschik Z, Ostaff MJ, Tiemessen MM, Staal FJ, Wang G, Gersemann M, Perminow G, Vatn MH, Schwab M, Stange EF, Wehkamp J. Beisner J, et al. Am J Physiol Gastrointest Liver Physiol. 2014 Sep 1;307(5):G487-98. doi: 10.1152/ajpgi.00347.2013. Epub 2014 Jul 3. Am J Physiol Gastrointest Liver Physiol. 2014. PMID: 24994854
-
Inflammatory bowel disease: an impaired barrier disease.
Jäger S, Stange EF, Wehkamp J. Jäger S, et al. Langenbecks Arch Surg. 2013 Jan;398(1):1-12. doi: 10.1007/s00423-012-1030-9. Epub 2012 Nov 18. Langenbecks Arch Surg. 2013. PMID: 23160753 Review.
-
Defensin deficiency, intestinal microbes, and the clinical phenotypes of Crohn's disease.
Wehkamp J, Schmid M, Fellermann K, Stange EF. Wehkamp J, et al. J Leukoc Biol. 2005 Apr;77(4):460-5. doi: 10.1189/jlb.0904543. Epub 2004 Dec 23. J Leukoc Biol. 2005. PMID: 15618294 Review.
Cited by
-
Belinson H, Savage AK, Fadrosh D, Kuo YM, Lin D, Valladares R, Nusse Y, Wynshaw-Boris A, Lynch SV, Locksley RM, Klein OD. Belinson H, et al. JCI Insight. 2016 Jul 7;1(10):e85395. doi: 10.1172/jci.insight.85395. JCI Insight. 2016. PMID: 27525310 Free PMC article.
-
Crohn's disease: Why the ileum?
Richard N, Savoye G, Leboutte M, Amamou A, Ghosh S, Marion-Letellier R. Richard N, et al. World J Gastroenterol. 2023 Jun 7;29(21):3222-3240. doi: 10.3748/wjg.v29.i21.3222. World J Gastroenterol. 2023. PMID: 37377591 Free PMC article. Review.
-
The broad pathogenetic role of TCF7L2 in human diseases beyond type 2 diabetes.
Del Bosque-Plata L, Hernández-Cortés EP, Gragnoli C. Del Bosque-Plata L, et al. J Cell Physiol. 2022 Jan;237(1):301-312. doi: 10.1002/jcp.30581. Epub 2021 Oct 6. J Cell Physiol. 2022. PMID: 34612510 Free PMC article. Review.
-
Genotype/phenotype analyses for 53 Crohn's disease associated genetic polymorphisms.
Jung C, Colombel JF, Lemann M, Beaugerie L, Allez M, Cosnes J, Vernier-Massouille G, Gornet JM, Gendre JP, Cezard JP, Ruemmele FM, Turck D, Merlin F, Zouali H, Libersa C, Dieudé P, Soufir N, Thomas G, Hugot JP. Jung C, et al. PLoS One. 2012;7(12):e52223. doi: 10.1371/journal.pone.0052223. Epub 2012 Dec 27. PLoS One. 2012. PMID: 23300620 Free PMC article.
-
Khaloian S, Rath E, Hammoudi N, Gleisinger E, Blutke A, Giesbertz P, Berger E, Metwaly A, Waldschmitt N, Allez M, Haller D. Khaloian S, et al. Gut. 2020 Nov;69(11):1939-1951. doi: 10.1136/gutjnl-2019-319514. Epub 2020 Feb 28. Gut. 2020. PMID: 32111634 Free PMC article.
References
-
- Podolsky DK. Inflammatory bowel disease. N Engl J Med. 2002;347:417–429. - PubMed
-
- Strober W. Immunology. Unraveling gut inflammation. Science. 2006;313:1052–1054. - PubMed
-
- Wehkamp J, Schmid M, Fellermann K, Stange EF. Defensin deficiency, intestinal microbes, and the clinical phenotypes of Crohn's disease. J Leukoc Biol. 2005;77:460–465. - PubMed
Publication types
MeSH terms
Substances
Grants and funding
LinkOut - more resources
Full Text Sources
Other Literature Sources
Medical